Adults with congenital heart disease (ACHD) represent an increasing proportion of non-cardiac surgical admissions and
might be at high risk for CV events. Pre-operative risk assessment in ACHD needs to focus on the underlying disease, type
of surgery, residua, and sequelae. Coexistence of HF, pulmonary hypertension, arrhythmia, hypoxaemia, damage to other or‐
gans, and endocarditis may considerably influence the baseline risk of these patients from no additional risk to very high
risk for worse prognosis. In a recent report, absolute mortality in ACHD patients undergoing NCS exceeded 4%. The classifi‐
cation in Table 9 is proposed for risk stratification.
Table 9 Risk stratification for non-cardiac surgery in adults with congenital heart disease
Patients with small, uncorrected defects, and no need for medication or any other
Minor risk treatment. Patients with successfully corrected CHD with no symptoms, no relevant
residua, and no need for medication
Patients with corrected or uncorrected conditions with residua
l haemodynamic ab‐
Intermediate risk
normality, with or without medication
Patients with uncorrected cyanotic heart disease, pulmonary hypertension, other
Severe risk complex congenital heart disease, ventricular dysfunction requiring medication, and
patients listed for heart transplantation
Recommendations for management of patients with adult congenital heart disease undergoing non-cardiac surgery
Recommendations Classa Levela
In patients with ACHD, a consultation by an ACHD specialist is rec‐
I C
ommended before intermediate-or high-risk surgery.
In patients with ACHD, it is recommended that intermediate-and
high-risk elective surgery is performed in a centre with experience in I C
the care of ACHD patients.
ACHD, Adults with congenital heart disease.
a
Class of recommendation and level of evidence as defined in Tables 1 and 2.